Angeborener Hörverlust · Sensorineural Deafness · Congenital Sensorineural Deafness · Erbliche Taubheit · Congenital Hereditary Sensorineural Deafness · Angeborene Taubheit · Pigmentassoziierte Taubheit
Congenital deafness is a hereditary hearing loss present from birth that affects the inner ear's sensory cells, preventing sound signals from reaching the brain. It is often linked to specific genetic variants, such as those associated with certain coat patterns like merle or piebald, or breed-specific conditions like Early Onset Adult Deafness (EOAD). This genetic defect causes the vital blood supply to the inner ear to fail, leading to the permanent degeneration of the hearing nerve cells.
Owners typically notice signs of deafness in early puppyhood, as affected dogs do not respond to sounds, sleep very deeply, and may startle easily when touched. Puppies might also bark unusually or fail to react to their littermates.
There is no cure for congenital deafness, making it a lifelong condition. While there are no direct medical treatments, owners typically spend between 100 and 1000 EUR on specialized training, hand-signal education, or safety aids like vibration collars.
Estimated range of typical treatment cost. Actual cost depends on severity, clinic and region.
More conditions affecting the Ears.